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Limited Cutaneous Systemic Sclerosis (ACA+) with Active Cutolo Pattern

Name: Limited Cutaneous Systemic Sclerosis (ACA+) with Active Cutolo Pattern
Creator: Gema María Lledó Ibáñez

Limited Cutaneous Systemic Sclerosis (ACA+)Active Cutolo Scleroderma PatternSevere

A 38-year-old woman with limited cutaneous systemic sclerosis, anti-centromere antibodies, and established active microangiopathy.

AuthorGema María Lledó Ibáñez

Clinical context

This case includes a 5-year history of Raynaud's phenomenon, esophageal dysmotility, and interstitial lung disease with an NSIP pattern, without current indirect echocardiographic signs of pulmonary hypertension.

Capillaroscopy

Capillaroscopy shows marked capillary loss (5.3/mm), frequent dilations, high prevalence of giant capillaries (27.5%), and hemorrhages, matching an active Cutolo pattern.

Key Capillaroscopic Findings

Marked capillary loss (5.3/mm)
High frequency of giant capillaries (27.5%)
Frequent capillary dilations (61.6%) with hemorrhages

Limited Cutaneous Systemic Sclerosis (ACA+) with Active Cutolo Pattern